Edit |   |
---|---|
Antigenic Specificity | Electron Transferring Flavoprotein Dehydrogenase (ETFDH) |
Clone | polyclonal |
Host Species | Rabbit |
Reactive Species | human |
Isotype | n/a |
Format | peptide affinity purified |
Size | 80 µl, 400 µl, |
Concentration | n/a |
Applications | ELISA, WB, IHC, FCM |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | Electron-transferring-flavoprotein dehydrogenase in the inner mitochondrial membrane accepts electrons from electron-transfer flavoprotein which is located in the mitochondrial matrix and reduces ubiquinone in the mitochondrial membrane. The protein is synthesized as a 67-kDa precursor which is targeted to mitochondria and processed in a single step to a 64-kDa mature form located in the mitochondrial membrane. Deficiency in electron-transferring-flavoprotein dehydrogenase have been demonstrated in some patients with type II glutaricacidemia. |
Immunogen | KLH-conjugated synthetic peptide between 32-61 amino acids from the N-terminal region of human ETFDH. |
Other Names | Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial, ETF-QO, ETF-ubiquinone oxidoreductase, Electron-transferring-flavoprotein dehydrogenase, ETF dehydrogenase, ETFDH, ETFQO, MADD, electron transfer flavoprotein ubiquinone oxidoreductase, Electron transfer flavoprotein-ubiquinone oxidoreductase, Electron transfer flavoprotein-ubiquinone oxidoreductase, Electron transfer flavoprotein-ubiquinone oxidoreductase , Electron transfer flavoprotein-ubiquinone oxidoreductase , mitochondrial, mitochondrial, mitochondrial , mitochondrial , ETF-QO, ETF-QO, ETF-QO , ETF-QO , ETF-ubiquinone oxidoreductase, ETF-ubiquinone oxidoreductase, ETF-ubiquinone oxidoreductase , ETF-ubiquinone oxidoreductase , Electron-transferring-flavoprotein dehydrogenase, Electron-transferring-flavoprotein dehydrogenase, Electron-transferring-flavoprotein dehydrogenase , Electron-transferring-flavoprotein dehydrogenase , ETF dehydrogenase, ETF dehydrogenase, ETF dehydrogenase , ETF dehydrogenase , |
Gene, Accession # | UniProt: Q16134 |
Catalog # | abx033036 |
Price | please inquire |
Order / More Info | Electron Transferring Flavoprotein Dehydrogenase (ETFDH) Antibody from ABBEXA LTD |
Product Specific References | n/a |
U.S. Office
118 Eldridge Rd, Suite C,
Sugar Land, TX 77478 USA
Telephone: +1 832 327 7413
Netherlands Office
Abbexa BV
Wattstraat 54 2723 RD,
Zoetermeer,Netherlands
Telephone: +44 (0) 1223 755950