2-Oxoisovalerate Dehydrogenase Subunit Beta, Mitochondrial (BCKDHB) Antibody from ABBEXA LTD
Search, find, compare suppliers for anti-2-Oxoisovalerate Dehydrogenase Subunit Beta, Mitochondrial (BCKDHB) antibody, protein, ELISA kits.
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| Antigenic Specificity | 2-Oxoisovalerate Dehydrogenase Subunit Beta, Mitochondrial (BCKDHB) |
| Clone | polyclonal |
| Host Species | Rabbit |
| Reactive Species | human |
| Isotype | n/a |
| Format | peptide affinity purified |
| Size | 80 µl, 400 µl, |
| Concentration | n/a |
| Applications | ELISA, WB, IHC, IF/ICC, FCM |
| Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
| Description | Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. |
| Immunogen | KLH-conjugated synthetic peptide between 41-70 amino acids from the N-terminal region of human BCKDHB. |
| Other Names | BCKDHB, 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial, Branched-chain alpha-keto acid dehydrogenase E1 component beta chain, BCKDHB, BCKDHB, BCKDHB , BCKDHB , 2-oxoisovalerate dehydrogenase subunit beta, 2-oxoisovalerate dehydrogenase subunit beta, 2-oxoisovalerate dehydrogenase subunit beta , 2-oxoisovalerate dehydrogenase subunit beta , mitochondrial, mitochondrial, mitochondrial , mitochondrial , Branched-chain alpha-keto acid dehydrogenase E1 component beta chain, Branched-chain alpha-keto acid dehydrogenase E1 component beta chain, Branched-chain alpha-keto acid dehydrogenase E1 component beta chain , Branched-chain alpha-keto acid dehydrogenase E1 component beta chain |
| Gene, Accession # | BCKDHB, UniProt: P21953 |
| Catalog # | abx025837 |
| Price | please inquire |
| Order / More Info | 2-Oxoisovalerate Dehydrogenase Subunit Beta, Mitochondrial (BCKDHB) Antibody from ABBEXA LTD |
| Product Specific References | n/a |
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