Edit |   |
---|---|
Antigenic Specificity | BCKDHB - N-terminal region |
Clone | polyclonal |
Host Species | Rabbit |
Reactive Species | cow, dog, horse, human, porcine, rabbit, rat |
Isotype | n/a |
Format | affinity purified |
Size | 0.1 mL |
Concentration | n/a |
Applications | Western Blot (WB) |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | This is a rabbit polyclonal antibody against BCKDHB. It was validated on Western BlotTarget Description: Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. Alternative splicing at th |
Immunogen | Immunogen: The immunogen is a synthetic peptide directed towards the N-terminal region of Human BCKDHB |
Other Names | [2-oxoisovalerate dehydrogenase subunit beta, mitochondrial; branched chain keto acid dehydrogenase E1 subunit beta] |
Gene, Accession # | [BCKDHB], Gene ID: 594, NCBI: Q5T2J3, UniProt: Q5T2J3 |
Catalog # | MBS3213969 |
Price | $365 |
Order / More Info | BCKDHB - N-terminal region Antibody from MYBIOSOURCE INC. |
Product Specific References | n/a |