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Antigenic Specificity | PEX5 |
Clone | polyclonal |
Host Species | Rabbit |
Reactive Species | human, mouse |
Isotype | n/a |
Format | affinity purified |
Size | 0.05 mL, 0.1 mL, 0.2 mL |
Concentration | n/a |
Applications | Western Blot (WB) |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | The product of this gene binds to the C-terminal PTS1-type tripeptide peroxisomal targeting signal (SKL-type) and plays an essential role in peroxisomal protein import. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the |
Immunogen | Immunogen: Recombinant protein of human PEX5 |
Other Names | [PBD2A; PBD2B; PTS1-BP; PTS1R; PXR1; RCDP5] |
Gene, Accession # | [PEX5], Gene ID: 5830, NCBI: P50542.3, UniProt: P50542 |
Catalog # | MBS9132386 |
Price | $200, $275, $430 |
Order / More Info | PEX5 Antibody from MYBIOSOURCE INC. |
Product Specific References | n/a |