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Antigenic Specificity | NEU1 |
Clone | polyclonal |
Host Species | Rabbit |
Reactive Species | human, mouse, rat |
Isotype | n/a |
Format | immunogen affinity purified |
Size | 0.1 mL |
Concentration | 1.0 mg/ml |
Applications | Western Blot (WB) |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | The antibody detects endogenous level of total NEU1 antibody. The protein encoded by this gene is a lysosomal enzyme that cleaves terminal sialic acid residues from substrates such as glycoproteins and glycolipids. In the lysosome, this enzyme is part of a heterotrimeric complex together with beta-galactosidase and cathepsin A (the latter is also referred to as 'protective protein'). Mutations in this gene can lead to sialidosis, a lysosomal storage disease that can be type 1 (cherry red spot-myoclonus syndrome or normosomatic type), which is late-onset, or type 2 (the dysmorphic type), which occurs at an earlier age with increased severity. |
Immunogen | Immunogen Type: Recombinant Protein Immunogen Description: Recombinant protein of human NEU1. |
Other Names | [NEU; NANH; SIAL1] |
Gene, Accession # | [NEU1], Gene ID: 4758, NCBI: NP_000425.1, UniProt: Q99519 |
Catalog # | MBS9405904 |
Price | $255 |
Order / More Info | NEU1 Antibody from MYBIOSOURCE INC. |
Product Specific References | n/a |