BCKDHB (N-term), 41-70 Antibody from MYBIOSOURCE INC.
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| Edit | |
|---|---|
| Antigenic Specificity | BCKDHB (N-term), 41-70 |
| Clone | polyclonal |
| Host Species | Rabbit |
| Reactive Species | human |
| Isotype | n/a |
| Format | peptide affinity purified |
| Size | 0.08 mL, 0.4 mL |
| Concentration | vial concentration: 0.45 |
| Applications | ELISA (EIA), Immunohistochemistry (IHC), Western Blot (WB), Flow Cytometry (FC/FACS), Immunofluorescence (IF) |
| Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
| Description | This BCKDHB antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 41-70 amino acids from the N-terminal region of human BCKDHB. Branched-chain keto acid dehydrogenase is a multienzymecomplex associated with the inner membrane of mitochondria, andfunctions in the catabolism of branched-chain amino acids. Thecomplex consists of multiple copies of 3 components: branched-chainalpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2)and lipoamide dehydrogenase (E3). This gene encodes the E1 betasubunit, and mutations therein have been associated with maplesyrup urine disease (MSUD), type 1B, a disease characterized by amaple syrup odor to the urine in addition to men |
| Immunogen | n/a |
| Other Names | [2-oxoisovalerate dehydrogenase subunit beta; mitochondrial; Branched-chain alpha-keto acid dehydrogenase E1 component beta chain; BCKDE1B; BCKDH E1-beta; BCKDHB] |
| Gene, Accession # | [BCKDHB], Gene ID: 594, NCBI: NP_000047.1, UniProt: P21953 |
| Catalog # | MBS9214739 |
| Price | $165, $370 |
| Order / More Info | BCKDHB (N-term), 41-70 Antibody from MYBIOSOURCE INC. |
| Product Specific References | Rose, J.E., et al. Mol. Med. 16 (7-8), 247-253 (2010) : Gorzelany, K., et al. Turk. J. Pediatr. 51(2):97-102(2009) Quental, S., et al. Mol. Genet. Metab. 94(2):148-156(2008) Kang, H., et al. Fertil. Steril. 89(3):728-731(2008) Flaschker, N., et al. J. Inherit. Metab. Dis. 30(6):903-909(2007) |
MYBIOSOURCE INC.
MYBIOSOURCE INC.
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P: 1.858.633.0165
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