Edit |   |
---|---|
Antigenic Specificity | COL6A2 (C-term), 719-747 |
Clone | polyclonal |
Host Species | Rabbit |
Reactive Species | human (predicted reactivity: mouse) |
Isotype | n/a |
Format | peptide affinity purified |
Size | 0.08 mL, 0.4 mL |
Concentration | vial concentration: 0.5 |
Applications | Western Blot (WB), ELISA (EIA) |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | This COL6A2 antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 719-747 amino acids from the C-terminal region of human COL6A2. COL6A2 is one of the three alpha chains of type VIcollagen, a beaded filament collagen found in most connectivetissues. The product of this gene contains several domains similarto von Willebrand Factor type A domains. These domains have beenshown to bind extracellular matrix proteins, an interaction thatexplains the importance of this collagen in organizing matrixcomponents. Mutations in this gene are associated with Bethlemmyopathy and Ullrich scleroatonic muscular dystrophy. Threetranscript variants have been identified for this gene. [provi |
Immunogen | n/a |
Other Names | [Collagen alpha-2(VI) chain; COL6A2] |
Gene, Accession # | [COL6A2], Gene ID: 1292, NCBI: NP_001840.3, UniProt: P12110 |
Catalog # | MBS9213043 |
Price | $165, $370 |
Order / More Info | COL6A2 (C-term), 719-747 Antibody from MYBIOSOURCE INC. |
Product Specific References | Zhang, R.Z., et al. J. Biol. Chem. 285(13):10005-10015(2010) Bovolenta, M., et al. BMC Med. Genet. 11, 44 (2010) : Chapuis, J., et al. Mol. Psychiatry 14(11):1004-1016(2009) Freise, C., et al. Matrix Biol. 28(8):480-489(2009) Martoni, E., et al. Hum. Mutat. 30 (5), E662-E672 (2009) : |