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Antigenic Specificity | ETFDH |
Clone | polyclonal |
Host Species | Rabbit |
Reactive Species | human. predicted: mouse, rat. |
Isotype | n/a |
Format | affinity purified |
Size | 0.1 mg |
Concentration | 100ug/100ul |
Applications | ELISA (EIA), Western Blot (WB), Immunohistochemistry (IHC) |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | This gene encodes a component of the electron-transfer system in mitochondria and is essential for electron transfer from a number of mitochondrial flavin-containing dehydrogenases to the main respiratory chain. Mutations in this gene are associated with glutaric acidemia. Alternatively spliced transcript variants that encode distinct isoforms have been observed. [provided by RefSeq, Aug 2013] |
Immunogen | Immunogen: Rabbit polyclonal ETFDH (1) antibody was raised against a recombinate human ETFDH protein 427-598 aa (BC011890). |
Other Names | n/a |
Gene, Accession # | [ETFDH] |
Catalog # | MBS415658 |
Price | $230 |
Order / More Info | ETFDH Antibody from MYBIOSOURCE INC. |
Product Specific References | (1) Wang,Z.Q., Chen,X.J., Murong,S.X. et al. Molecular analysis of 51 unrelated pedigrees with late-onset multiple acyl-CoA dehydrogenation deficiency (MADD) in southern China confirmed the most common ETFDH mutation and high carrier frequency of c.250G>A. J. Mol. Med. 89 (6), 569-576 (2011). |